Science and Innovations in MedicineScience and Innovations in MedicineНаука и инновации в медицине2500-13882618-754XFSBEI of Higher Education SamSMU of Ministry of Health of the Russian Federation5301610.35693/2500-1388-2020-5-4-235-238CardiologyКардиологияResearch ArticleAcquired long QT syndrome caused by pseudohypoparathyroidismВторичный синдром удлиненного интервала QT в результате псевдогипопаратиреозаhttps://orcid.org/0000-0002-2290-0013BalykovaL. A.БалыковаЛ. А.
Russian Federation

PhD, Professor, Associate Member of RAS, the Head of the Department of Pediatrics, the Director of Medical Institute

д.м.н., профессор, чл.-корр. РАН, зав. кафедрой педиатрии, директор Медицинского института

larisabalykova@yandex.ruhttps://orcid.org/0000-0002-8192-7902SamoshkinaE. S.СамошкинаЕ. С.
Russian Federation

PhD, Associate Professor, Department of Pediatrics of Medical Institute

к.м.н., доцент кафедры педиатрии Медицинского института

larisabalykova@yandex.ruPetrushkinaYu. A.ПетрушкинаЮ. А.
Russian Federation

the Acting head of Cardiology Department

и.о. зав. отделением кардиологии

larisabalykova@yandex.ruhttps://orcid.org/0000-0002-2548-9303ZolnikovaT. M.ЗольниковаТ. М.
Russian Federation

resident of the Department of Pediatrics of Medical Institute

ординатор кафедры педиатрии Медицинского института

larisabalykova@yandex.ruhttps://orcid.org/0000-0003-3990-9353KrasnopolskayaA. V.КраснопольскаяА. В.
Russian Federation

assistant of the Department of Pediatrics of Medical Institute

ассистент кафедры педиатрии Медицинского института

larisabalykova@yandex.ruBlohinaS. I.БлохинаС. И.
Russian Federation

student of Medical Institute

студентка Медицинского института

larisabalykova@yandex.ruOgarev Mordovia State UniversityФГБОУ ВО «Национальный исследовательский Мордовский государственный университет имени Н.П. Огарева»Mordovia Republican Children’s Clinical HospitalГБУЗ Республики Мордовия «Детская республиканская клиническая больница»07122020542352380512202005122020Copyright ©; 2020, Balykova L.A., Samoshkina E.S., Petrushkina Y.A., Zolnikova T.M., Krasnopolskaya A.V., Blohina S.I.Copyright ©; 2020, Балыкова Л.А., Самошкина Е.С., Петрушкина Ю.А., Зольникова Т.М., Краснопольская А.В., Блохина С.И.2020Balykova L.A., Samoshkina E.S., Petrushkina Y.A., Zolnikova T.M., Krasnopolskaya A.V., Blohina S.I.Балыкова Л.А., Самошкина Е.С., Петрушкина Ю.А., Зольникова Т.М., Краснопольская А.В., Блохина С.И.https://creativecommons.org/licenses/by/4.0https://innoscience.ru/2500-1388/article/view/53016

The article presents a review of literature data on the long QT syndrome (LQTS), focusing on the role of secondary factors in the development of this disorder. In particular, it describes in detail pseudohypoparathyroidism – a rare genetically and clinically heterogeneous condition characterized by resistance to parathyroid hormone, often manifested by arrhythmogenic syncope and seizures. A specific clinical case illustrates the necessity to exclude the endocrine and electrolyte abnormalities in syncopal conditions associated with the QT interval prolongation.

Представлен обзор литературы по проблеме синдрома удлиненного интервала QT (СУИQT). Раскрыта роль вторичных причин в развитии заболевания. В частности, подробно описан псевдогипопаратиреоз – редкое генетически и клинически гетерогенное заболевание, характеризующееся резистентностью к паратгормону, часто манифестирующее аритмогенными синкопе и судорогами. На конкретном клиническом примере показана необходимость исключения эндокринных и электролитных нарушений при синкопальных состояниях, ассоциированных с удлинением QT.

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